Cor triatriatum sinister- rare congenital heart disease - our experiences in the diagnosis and treatment in childhood
- Cor triatriatum sinister,
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Cor triatriatum sinister is a rare congenital heart defect in which left atrium is divided in two parts with the fibromuscular membrane. The proximal atrium accepts the pulmonary veins with their blood flow, the distal or (real) atrium is usually empty and separated from the ventricle by the mitral valve. There is a constant communication between the two parts of the divided atrium by which the blood flow is redirected to the left ventricle. This defect is rare, usually isolated, but it might be combined with other congenital heart defects. We present cases of two children aged 8 and 3 years at the time of establishment the diagnosis. In both cases the main clinical signs were fatigue and heart murmur on auscultation. Anamnesis, clinical symptoms and signs, ECG, chest X ray and the gold standard – echocardiography were used for establishing the diagnosis. Definitive treatment was made with cardiosurgical resection of the fibromuscular membrane using extracorporeal circulation. Regular periodical evaluation is necessary in order to discover late complications of cardiac rhythm disturbances
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